What is the diagnosis for a 4-week-old male infant with hypoplastic left heart syndrome (HLHS) presenting with fever, hypotension, tachycardia, tachypnea, and hypoxemia, following palliative heart surgery?

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Differential Diagnosis for a 4-week-old Male Infant with Hypoplastic Left Heart Syndrome

  • Single most likely diagnosis:
    • Sepsis: The infant's symptoms of fever (38.3 C), tachycardia (175/min), tachypnea (70/min), and hypoxia (pulse oximetry 80% on room air) are highly suggestive of sepsis, a common and serious complication in post-surgical patients, especially those with complex congenital heart disease.
  • Other Likely diagnoses:
    • Cardiac failure: Given the patient's history of hypoplastic left heart syndrome and recent palliative heart surgery, cardiac failure is a plausible diagnosis, as the infant may be experiencing decreased cardiac output or fluid overload.
    • Respiratory infection: The symptoms of tachypnea, tachycardia, and hypoxia could also indicate a respiratory infection, which is a common complication in infants with congenital heart disease.
    • Gastroesophageal reflux disease (GERD): The episode of vomiting could be related to GERD, which is common in infants, especially those with congenital heart disease.
  • Do Not Miss (ddxs that may not be likely, but would be deadly if missed.):
    • Cardiac tamponade: Although less likely, cardiac tamponade is a life-threatening condition that can occur after cardiac surgery, and the distant heart sounds and hypotension (80/40 mm Hg) make it a diagnosis that should not be missed.
    • Pulmonary embolism: Although rare in infants, pulmonary embolism can occur, especially in patients with central venous catheters or recent surgery, and would be catastrophic if not recognized and treated promptly.
  • Rare diagnoses:
    • Coronary artery thrombosis: This is a rare but potentially life-threatening complication that can occur after cardiac surgery, especially in patients with complex congenital heart disease.
    • Myocardial ischemia: Myocardial ischemia can occur in infants with congenital heart disease, especially after cardiac surgery, and would require prompt recognition and treatment to prevent long-term damage.

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This information is intended for healthcare professionals. Any medical decision-making should rely on clinical judgment and independently verified information. The content provided herein does not replace professional discretion and should be considered supplementary to established clinical guidelines. Healthcare providers should verify all information against primary literature and current practice standards before application in patient care. Dr.Oracle assumes no liability for clinical decisions based on this content.

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