What biotin-dependent enzyme is active during fasting and contributes to gluconeogenesis?

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From the Guidelines

Pyruvate carboxylase is the key biotin-dependent enzyme that becomes active during fasting and contributes significantly to gluconeogenesis. This enzyme catalyzes the conversion of pyruvate to oxaloacetate, which is the first committed step in the gluconeogenesis pathway [ 1 ]. During fasting, when blood glucose levels drop, pyruvate carboxylase activity increases to help maintain blood glucose homeostasis by promoting the synthesis of new glucose from non-carbohydrate precursors. The enzyme requires biotin as an essential cofactor to function properly, as biotin serves as a carrier for carbon dioxide in the carboxylation reaction.

Some key points about pyruvate carboxylase include:

  • It is primarily located in the mitochondria of liver and kidney cells, where most gluconeogenesis occurs [ 1 ]
  • Its activity is upregulated during fasting by increased levels of acetyl-CoA (which accumulates during fatty acid oxidation) and by hormones like glucagon and cortisol, which are elevated during fasting states
  • Biotin deficiency can impair pyruvate carboxylase activity and consequently reduce gluconeogenesis capacity, potentially leading to hypoglycemia during fasting periods [ 1 ]

The biotin cycle, as described in [ 1 ], highlights the importance of biotin in various metabolic processes, including gluconeogenesis, fatty acid synthesis, and amino acid catabolism. The cycle involves the conversion of dietary biotin into active holocarboxylases, which are then degraded to produce free biotin that can be recycled. This process ensures a continuous supply of biotin for various biotin-dependent enzymes, including pyruvate carboxylase.

In the context of fasting, the activation of pyruvate carboxylase is crucial for maintaining blood glucose levels, and any impairment in its activity due to biotin deficiency can have significant consequences for glucose homeostasis [ 1 ]. Therefore, it is essential to ensure adequate biotin intake, especially during periods of fasting or when glucose homeostasis is critical.

From the Research

Biotin-Dependent Enzymes and Fasting

  • Pyruvate carboxylase (PC) is a biotin-dependent enzyme that plays a crucial role in gluconeogenesis, lipogenesis, and amino acid catabolism 2, 3, 4.
  • During fasting, pyruvate carboxylase is active and contributes to gluconeogenesis, which is the process of generating glucose from non-carbohydrate sources 5.

Role of Pyruvate Carboxylase in Gluconeogenesis

  • Pyruvate carboxylase catalyzes the carboxylation of pyruvate to form oxaloacetate, which is a critical step in gluconeogenesis 3, 4.
  • The enzyme is allosterically regulated by acetyl-CoA and aspartate, and its activity is essential for maintaining blood glucose levels during fasting and other physiological states 5, 3.

Importance of Biotin for Pyruvate Carboxylase Activity

  • Biotin is a cofactor for pyruvate carboxylase, and its deficiency can lead to reduced enzyme activity and impaired gluconeogenesis 2, 6.
  • Biotin deficiency can also affect the synthesis and degradation of pyruvate carboxylase, leading to reduced enzyme mass and activity 2.

References

Professional Medical Disclaimer

This information is intended for healthcare professionals. Any medical decision-making should rely on clinical judgment and independently verified information. The content provided herein does not replace professional discretion and should be considered supplementary to established clinical guidelines. Healthcare providers should verify all information against primary literature and current practice standards before application in patient care. Dr.Oracle assumes no liability for clinical decisions based on this content.

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