What is the diagnostic algorithm for Calcium Pyrophosphate Deposition Disease (CPPD), also known as pseudogout?

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Last updated: May 26, 2025View editorial policy

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From the Guidelines

Pseudogout diagnosis and management should start with X-ray of the area of interest to identify characteristic findings such as chondrocalcinosis and calcification of tendons, ligaments, and joint capsules, as recommended by the American College of Radiology with a rating of 9 1. The diagnosis of pseudogout is crucial for appropriate management, and imaging plays a significant role in this process. According to the American College of Radiology, X-ray of the area of interest is the most appropriate initial imaging procedure for suspected pseudogout, with a rating of 9, indicating that it is usually appropriate 1. This is because X-ray can effectively demonstrate soft tissue calcification, chondrocalcinosis, and osseous changes associated with pseudogout.

Key Considerations for Pseudogout Management

  • Confirming the diagnosis through joint fluid analysis showing calcium pyrophosphate crystals
  • First-line treatment for acute attacks includes NSAIDs like naproxen or indomethacin for 7-14 days
  • Colchicine is an effective alternative for acute attacks, starting with 1.2mg followed by 0.6mg one hour later, then 0.6mg once or twice daily until symptoms resolve
  • For patients with contraindications to these medications, joint aspiration followed by intra-articular corticosteroid injection provides targeted relief
  • Systemic corticosteroids like prednisone can be used for polyarticular attacks or when other options aren't suitable
  • For prophylaxis in patients with recurrent attacks, low-dose colchicine may be beneficial

Imaging Recommendations

  • X-ray of the area of interest is the preferred initial imaging procedure due to its high rating of 9 1
  • CT and MRI may also be used to identify chondrocalcinosis and calcification, but they have lower ratings of 5 1
  • Ultrasound can be used to evaluate the area of interest, but it also has a rating of 5 1

Underlying Conditions

  • Addressing underlying conditions like hyperparathyroidism or hemochromatosis is crucial as these can contribute to calcium pyrophosphate deposition 1
  • Management of these conditions should follow existing guidelines or recommendations, which are not reviewed here 1

Treatment Objectives

  • The objectives of management are to relieve symptoms and to prevent acute attacks 1
  • Disease-modifying treatments have yet to be developed, and research evidence to support the recommendations is sparse 1

From the Research

Pseudogout Algorithm

The management of pseudogout involves both acute and long-term treatment strategies.

  • Acute treatment is similar to that of gouty arthritis, focusing on relieving symptoms of joint inflammation 2.
  • There is no standard regimen for long-term chronic therapies of pseudogout, unlike gout where urate-lowering therapy is used to prevent recurrent attacks 2.

Treatment Approaches

Current treatment approaches for pseudogout are mainly directed at relieving the symptoms of joint inflammation.

  • Colchicine can be used as a prophylactic agent in managing recurrent attacks, and its effects on the NACHT, LRR and PYD domains-containing protein 3 (NALP-3) inflammasome of the innate immune system are highlighted 3.
  • Agents that directly target the inflammasome, such as drugs which inhibit the interleukin 1 pathway, can be used in the treatment of severe, refractory pseudogout 3.

Comparison with Gout Treatment

While gout treatment often involves urate-lowering therapy to prevent recurrent attacks, pseudogout treatment does not have a similar approach.

  • A study comparing naproxen and low-dose colchicine for the treatment of gout flares found no significant difference in pain intensity between the two groups, but naproxen caused fewer side effects 4.
  • The treatment of pseudogout is often focused on managing symptoms and preventing further attacks, rather than addressing the underlying cause of the disease 5, 2, 3.

References

Professional Medical Disclaimer

This information is intended for healthcare professionals. Any medical decision-making should rely on clinical judgment and independently verified information. The content provided herein does not replace professional discretion and should be considered supplementary to established clinical guidelines. Healthcare providers should verify all information against primary literature and current practice standards before application in patient care. Dr.Oracle assumes no liability for clinical decisions based on this content.

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