What is the expected von Willebrand's antigen to activity ratio in a person with normal clotting?

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Von Willebrand's Antigen to Activity Ratio in Normal Clotting

In a person with normal clotting, the von Willebrand's antigen to activity ratio (VWF:RCo/VWF:Ag or VWF:Act/VWF:Ag) should be between 0.7-1.2. 1, 2

Normal Ratio Values

The normal ratio of von Willebrand factor activity to antigen has been established through multiple studies:

  • In healthy subjects, the reference range for VWF:Act/VWF:Ag is 0.8-1.16 2
  • In normal patients (with normal multimers), the reference range for VWF:Act/VWF:Ag is 0.73-1.14 2
  • For VWF:RCo/VWF:Ag, the reference ranges are:
    • 0.74-1.23 in healthy individuals
    • 0.62-1.25 in normal patients 2

Clinical Significance of the Ratio

The VWF activity to antigen ratio is a critical parameter in:

  1. Differentiating VWD types:

    • Type 1 VWD typically has a normal ratio (approximately 1) with reduced levels of both antigen and activity
    • Type 2 VWD variants (2A, 2B, 2M) typically show a reduced ratio (<0.7) 1, 3
  2. Detecting acquired von Willebrand syndrome (AVWS):

    • A decreased ratio (<0.7) is indicative of AVWS 4, 5
    • In patients on ECMO support, the ratio typically decreases to around 0.52-0.64 5

Diagnostic Cutoffs

The recommended cutoff ratio for distinguishing normal from abnormal VWF function varies slightly by guideline:

  • Most commonly, a ratio <0.7 is considered abnormal 1, 3
  • Some guidelines use a more stringent cutoff of <0.5-0.6 3
  • For Type 2 VWD subtypes (2A, 2B, 2M), the ratio is typically <0.5-0.7 1

Technical Considerations

When interpreting VWF ratios, consider:

  • Test variability can affect the ratio calculation
  • VWF:Act assays may have better precision than VWF:RCo assays 2
  • Multiple tests may be needed for accurate diagnosis, especially in borderline cases
  • Patient factors like stress, exercise, pregnancy, and inflammation can affect VWF levels 1

Clinical Application

A normal ratio (≥0.7) in a person with good clotting indicates:

  • Normal VWF function
  • Normal multimer structure
  • Absence of qualitative VWF defects

If the ratio is abnormal (<0.7) despite normal clotting history, further evaluation may be warranted, including:

  • VWF multimer analysis
  • Specialized platelet function studies
  • Assessment of other coagulation factors 1

Remember that a single normal test does not definitively rule out all bleeding disorders, and clinical correlation is essential when interpreting laboratory results.

References

Guideline

Bleeding Disorder Diagnosis

Praxis Medical Insights: Practical Summaries of Clinical Guidelines, 2025

Guideline

Guideline Directed Topic Overview

Dr.Oracle Medical Advisory Board & Editors, 2025

Professional Medical Disclaimer

This information is intended for healthcare professionals. Any medical decision-making should rely on clinical judgment and independently verified information. The content provided herein does not replace professional discretion and should be considered supplementary to established clinical guidelines. Healthcare providers should verify all information against primary literature and current practice standards before application in patient care. Dr.Oracle assumes no liability for clinical decisions based on this content.

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