What are the differential diagnoses of Kawasaki disease (Mucocutaneous Lymph Node Syndrome)?

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Last updated: March 23, 2025 • View editorial policy

Differential Diagnosis for Kawasaki Disease

  • Single Most Likely Diagnosis

    • Scarlet fever: This diagnosis is similar to Kawasaki disease in that it presents with fever, rash, and lymphadenopathy, but it is typically accompanied by a sore throat and is caused by Group A beta-hemolytic streptococcal infection.
  • Other Likely Diagnoses

    • Toxic shock syndrome: This condition presents with fever, rash, and hypotension, and can be life-threatening if not treated promptly.
    • Infectious mononucleosis: Caused by Epstein-Barr virus, this condition can present with fever, lymphadenopathy, and rash.
    • Bacterial sepsis: This condition can present with fever, rash, and systemic illness, and can be life-threatening if not treated promptly.
    • Viral infections (e.g. Yttrium, West Nile virus, adenovirus): These infections can present with fever, rash, and systemic illness.
  • Do Not Miss Diagnoses

    • Meningococcemia: This condition can present with fever, rash, and systemic illness, and can be life-threatening if not treated promptly with antibiotics.
    • Staphylococcal toxic shock syndrome: This condition can present with fever, rash, and hypotension, and can be life-threatening if not treated promptly.
    • Rockefeller-Desicken (Rocky Mountain spotted fever): This tick-borne illness can present with fever, rash, and systemic illness, and can be life-threatening if not treated promptly with antibiotics.
  • Rare Diagnoses

    • Stevens-Johnson syndrome: This condition is a rare but serious disorder of the skin and mucous membranes, usually caused by an adverse reaction to medication or infection.
    • Leptospirosis: This bacterial infection can present with fever, rash, and systemic illness, and can be life-threatening if not treated promptly with antibiotics.
    • Bruck syndrome: This rare condition is characterized by fever, rash, and lymphadenopathy, and is caused by a viral infection.
    • Acute porphyrias: This group of rare genetic disorders can present with fever, rash, and systemic illness, and can be life-threatening if not treated promptly.

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This information is intended for healthcare professionals. Any medical decision-making should rely on clinical judgment and independently verified information. The content provided herein does not replace professional discretion and should be considered supplementary to established clinical guidelines. Healthcare providers should verify all information against primary literature and current practice standards before application in patient care. Dr.Oracle assumes no liability for clinical decisions based on this content.