From the Research
Auricle dysplasia is a congenital abnormality affecting the development of the external ear, involving malformation of the ear's cartilage and skin, and can range from minor structural irregularities to complete absence of the external ear (anotia) 1. This condition can occur on one side (unilateral) or both sides (bilateral) and can be associated with other conditions such as microtia (small ear), hemifacial microsomia, or various genetic syndromes including Treacher Collins syndrome and CHARGE syndrome. The underlying cause is typically disruption of normal embryonic development during the first trimester of pregnancy, which may result from genetic factors, environmental exposures, or a combination of both 2. While mild cases might require no treatment, more significant dysplasia often requires surgical reconstruction, which may involve multiple procedures starting around 6-10 years of age 3. Some patients may benefit from prosthetic ears or hearing aids if hearing is affected. Early evaluation by a multidisciplinary team including otolaryngologists, plastic surgeons, and audiologists is important for optimal management 4. Key considerations in the management of auricle dysplasia include:
- Accurate diagnosis and classification of the anomaly
- Assessment of hearing and middle ear function
- Surgical reconstruction or other interventions as needed
- Multidisciplinary care and support for affected individuals and their families. It is essential to prioritize a comprehensive approach to managing auricle dysplasia, considering the potential impact on the individual's quality of life, morbidity, and mortality 5.