Evaluation and Management of a 2-Year-Old Hearing Clicking, High-Pitched Noises
Any parental concern about hearing loss or auditory symptoms in a 2-year-old must be taken seriously and requires immediate objective hearing screening and comprehensive audiologic evaluation. 1
Immediate Action Required
Perform objective hearing screening immediately – parental concerns about hearing warrant prompt evaluation regardless of whether the child passed newborn screening. 1 The clicking/high-pitched noises the child is experiencing could represent:
- Tinnitus (the child perceiving sounds)
- Objective sounds (audible clicking from palatal myoclonus or middle ear pathology) 2
- Symptoms of underlying hearing loss
Diagnostic Approach
1. Targeted History and Physical Examination
Obtain specific information about:
- Onset, duration, laterality (one ear vs. both ears) of the clicking sounds
- Whether sounds are continuous or intermittent, present during sleep
- Whether YOU can hear the clicking (objective vs. subjective tinnitus)
- Associated symptoms: hearing difficulty, speech delay, ear pain, vertigo, sensation of blocked ear 3
- Risk factors for hearing loss 1:
- Family history of childhood hearing loss
- History of NICU stay >5 days, ototoxic medications, hyperbilirubinemia
- In utero infections (CMV, toxoplasmosis, rubella)
- Craniofacial anomalies
- Recurrent or persistent otitis media ≥3 months
- Head trauma
- Neurodegenerative disorders or syndromes
Physical examination must include:
- Pneumatic otoscopy to assess tympanic membrane and middle ear status 1
- Examination for craniofacial anomalies, ear tags, pits
- Direct observation of soft palate during vocalization (palatal myoclonus causes audible clicking) 2
- Neurological examination for focal deficits
2. Objective Hearing Assessment
Refer immediately to pediatric audiologist for comprehensive audiologic examination 1, 4. At age 2, this should include:
- Auditory brainstem response (ABR) testing – essential for confirming hearing status in young children 4
- Tympanometry to assess middle ear function 1
- Age-appropriate behavioral audiometry
Do not delay this referral – children with risk factors or parental concerns require diagnostic audiology assessment by 24-30 months of age at the latest. 1, 4
3. Otolaryngology Referral
Refer to pediatric otolaryngologist for evaluation of:
- Structural ear abnormalities
- Chronic otitis media with effusion (leading cause of acquired hearing loss) 1
- Palatal myoclonus (if clicking is audible to examiner) 2
- Cerumen impaction requiring removal 1
4. Imaging – Only If Indicated
Do NOT routinely obtain imaging unless specific findings are present 5:
- Unilateral symptoms
- Focal neurological abnormalities
- Asymmetric hearing loss on audiometry
- Pulsatile quality to sounds
Common Pitfalls to Avoid
- Never dismiss parental concerns – this is explicitly emphasized as a key principle 1
- Don't assume passed newborn screening means no hearing problem – delayed-onset and progressive hearing loss occurs 1, 4
- Don't use tympanometry or otoscopy alone – these assess middle ear status but do not assess hearing 1
- Don't wait for speech delay to develop – hearing loss must be identified and treated before language impact occurs 4
Management Based on Findings
If hearing loss confirmed:
- Intervention within 1 month of diagnosis 4
- Hearing aids for mild-moderate loss
- Consider cochlear implant evaluation for severe-profound bilateral loss
- Genetics consultation 4
- Ophthalmology evaluation 4
- Early intervention services 4
If otitis media with effusion present:
- Hearing testing when OME persists ≥3 months 6
- Re-examination every 3-6 months until resolved 6
- Consider tympanostomy tubes if persistent with hearing loss 6
If palatal myoclonus identified:
- This is a benign localized movement disorder causing objective clicking 2
- Typically not continuous, ceases during sleep
- May be volitionally controlled by the child
- MRI to exclude anatomical causes if diagnosis uncertain 2
The critical message: immediate audiologic referral is mandatory – this 2-year-old requires comprehensive hearing assessment regardless of the ultimate cause of the clicking sounds, because any auditory symptom with parental concern warrants definitive evaluation. 1