What is the most likely cause of congenital hypothyroidism in a 1-month-old boy with elevated Thyroid-Stimulating Hormone (TSH) levels, low serum Thyroxine (T4) levels, jaundice, a large protruding tongue, and a hoarse cry?

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Differential Diagnosis for the 1-month-old Boy

The patient's presentation of scleral icterus, jaundice, large protruding tongue, hoarse cry, and laboratory results indicating elevated TSH and low T4 levels suggest a diagnosis of congenital hypothyroidism. Here is the differential diagnosis organized into categories:

  • Single most likely diagnosis
    • D. Thyroid dysgenesis: This is the most common cause of congenital hypothyroidism, accounting for approximately 80% of cases. The patient's symptoms and laboratory results are consistent with this diagnosis.
  • Other Likely diagnoses
    • A. Defective thyroid peroxidase activity: This is a possible cause of congenital hypothyroidism, although less common than thyroid dysgenesis. It is an autosomal recessive disorder that affects the production of thyroid hormones.
    • E. Transplacental TSH receptor–stimulating antibody: This is a rare cause of congenital hypothyroidism, but it can occur in infants born to mothers with Graves' disease.
  • Do Not Miss (ddxs that may not be likely, but would be deadly if missed.)
    • C. Panhypopituitarism: Although less likely, panhypopituitarism can present with similar symptoms, including hypothyroidism, and is a life-threatening condition if left untreated.
  • Rare diagnoses
    • B. Iodine deficiency (endemic goiter): This is unlikely in this case, as the mother consumed a well-balanced diet and took prenatal vitamins throughout the pregnancy, suggesting adequate iodine intake. However, it is still a possible cause of congenital hypothyroidism in areas with endemic iodine deficiency.

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This information is intended for healthcare professionals. Any medical decision-making should rely on clinical judgment and independently verified information. The content provided herein does not replace professional discretion and should be considered supplementary to established clinical guidelines. Healthcare providers should verify all information against primary literature and current practice standards before application in patient care. Dr.Oracle assumes no liability for clinical decisions based on this content.

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