From the Research
The ICD-10 code for sickle cell disease is D57, as indicated in the most recent study 1. This code is used to represent sickle cell disease in general, with several more specific subcodes depending on the exact type and manifestations of the disease.
- The main code D57.1 represents sickle cell disease without crisis,
- while D57.0 indicates sickle cell anemia with crisis. For more specific documentation,
- D57.2 is used for double heterozygous sickling disorders,
- D57.3 for sickle cell trait,
- D57.4 for sickle cell thalassemia,
- and D57.8 for other sickle cell disorders. When coding sickle cell disease, it's essential to document any acute complications or crises with additional codes, such as D57.00 for vaso-occlusive crisis or D57.01 for acute chest syndrome, as supported by recent research 2. Proper coding is crucial for accurate medical records, appropriate reimbursement, and tracking disease prevalence. Sickle cell disease is a genetic blood disorder characterized by abnormal hemoglobin that causes red blood cells to become rigid and sickle-shaped, leading to vascular occlusion, chronic hemolytic anemia, and organ damage, as described in 3 and 4. The importance of accurate coding is further emphasized by the need for standardized codes for complications and comorbidities associated with sickle cell disease, as highlighted in 2. Overall, the use of the ICD-10 code D57 and its subcodes is essential for effective management and tracking of sickle cell disease, as supported by the latest evidence 1, 2.