What are the diagnostic criteria for DRESS (Drug Reaction with Eosinophilia and Systemic Symptoms) syndrome?

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Differential Diagnosis for DRESS Syndrome

Single Most Likely Diagnosis

  • DRESS Syndrome (Drug Reaction with Eosinophilia and Systemic Symptoms): This is the most likely diagnosis given the context of the question. DRESS syndrome is a severe skin and systemic reaction to medications, characterized by fever, rash, lymphadenopathy, and internal organ involvement, often accompanied by eosinophilia.

Other Likely Diagnoses

  • Stevens-Johnson Syndrome (SJS) and Toxic Epidermal Necrolysis (TEN): These conditions are also severe skin reactions, often drug-induced, but they primarily involve the skin and mucous membranes, with less emphasis on systemic symptoms like eosinophilia and lymphadenopathy compared to DRESS.
  • Acute Generalized Exanthematous Pustulosis (AGEP): This is a skin condition characterized by numerous small, sterile pustules on a background of erythema, often triggered by medications. While it can be severe, it tends to have fewer systemic symptoms than DRESS.
  • Hypersensitivity Vasculitis: This condition involves inflammation of blood vessels and can be triggered by drugs, among other causes. It presents with skin lesions, but systemic involvement can vary.

Do Not Miss Diagnoses

  • Sepsis: Although less likely to present with the specific constellation of symptoms seen in DRESS, sepsis is a life-threatening condition that can cause fever, rash, and organ dysfunction. It must be considered, especially if the patient shows signs of severe infection.
  • Malignant Lymphoma: Certain types of lymphoma can present with systemic symptoms, lymphadenopathy, and skin lesions, making them important to rule out, especially in patients with persistent or unexplained symptoms.
  • Autoimmune Disorders (e.g., Lupus, Rheumatoid Arthritis): These conditions can cause a wide range of systemic symptoms, including skin rashes, fever, and lymphadenopathy, and must be considered in the differential diagnosis.

Rare Diagnoses

  • Eosinophilia-Myalgia Syndrome: A rare condition associated with the ingestion of contaminated tryptophan supplements, characterized by severe muscle pain and elevated eosinophil counts.
  • Churg-Strauss Syndrome (Eosinophilic Granulomatosis with Polyangiitis): A rare autoimmune condition that involves asthma, high levels of eosinophils, and vasculitis. It can present with skin lesions, fever, and systemic symptoms.
  • Histiocytosis: A group of rare diseases involving abnormal proliferation of histiocytes, which can cause a variety of systemic symptoms, including skin lesions and organ dysfunction.

Professional Medical Disclaimer

This information is intended for healthcare professionals. Any medical decision-making should rely on clinical judgment and independently verified information. The content provided herein does not replace professional discretion and should be considered supplementary to established clinical guidelines. Healthcare providers should verify all information against primary literature and current practice standards before application in patient care. Dr.Oracle assumes no liability for clinical decisions based on this content.

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