What is the laboratory workup for autoimmune hepatitis (AIH)?

Medical Advisory BoardAll articles are reviewed for accuracy by our Medical Advisory Board
Educational purpose only • Exercise caution as content is pending human review
Article Review Status
Submitted
Under Review
Approved

Last updated: March 4, 2025View editorial policy

Personalize

Help us tailor your experience

Which best describes you? Your choice helps us use language that's most understandable for you.

From the Guidelines

Laboratory workup for autoimmune hepatitis should include liver function tests, complete blood count, and specific autoimmune markers, with the most important serological tests being antinuclear antibodies (ANA), anti-smooth muscle antibodies (ASMA), liver-kidney microsomal type 1 antibodies (anti-LKM1), and immunoglobulin G (IgG) levels, as recommended by the most recent guidelines 1. The diagnosis of autoimmune hepatitis (AIH) is based on a combination of clinical, laboratory, and histological findings. The laboratory workup should include:

  • Liver function tests: ALT, AST, alkaline phosphatase, GGT, bilirubin
  • Complete blood count
  • Specific autoimmune markers:
    • Antinuclear antibodies (ANA)
    • Anti-smooth muscle antibodies (ASMA)
    • Liver-kidney microsomal type 1 antibodies (anti-LKM1)
    • Immunoglobulin G (IgG) levels Additional tests should include:
  • Anti-soluble liver antigen (anti-SLA)
  • Anti-liver cytosol type 1 (anti-LC1)
  • Perinuclear anti-neutrophil cytoplasmic antibodies (pANCA) Viral hepatitis markers (HBV, HCV) should be checked to exclude viral causes. A liver biopsy is often necessary for definitive diagnosis, showing interface hepatitis, lymphoplasmacytic infiltration, and other characteristic features. Patients should also be evaluated for concurrent autoimmune conditions like thyroid disease, celiac disease, and inflammatory bowel disease. The diagnosis of AIH is based on a scoring system that considers laboratory abnormalities, histological findings, and exclusion of other liver diseases, as outlined in the guidelines 1. Early diagnosis is crucial as prompt immunosuppressive therapy can prevent progression to cirrhosis and liver failure. The most recent guidelines recommend using the simplified diagnostic criteria for AIH, which include increased serum IgG levels, presence of ANA, SMA, or LKM-1, and compatible liver histology 1.

From the Research

Laboratory Workup for Autoimmune Hepatitis (AIH)

The laboratory workup for AIH involves several tests, including:

  • Autoantibody detection, which is mandatory for AIH diagnosis and classification 2
  • Serum globulin level tests, which are often elevated in AIH patients 3, 4
  • Liver enzyme level tests, such as aspartate and alanine aminotransferase, which are often increased in AIH patients 5, 3
  • Immunoglobulin G level tests, which are often increased in AIH patients 5, 3

Autoantibody Detection

Autoantibody detection is a crucial part of the laboratory workup for AIH, with different autoantibodies associated with different types of AIH:

  • Type 1 AIH is characterized by seropositivity for smooth muscle and/or antinuclear antibodies 3, 4
  • Type 2 AIH is characterized by positivity for liver kidney microsomal type 1 antibodies 3, 4

Diagnostic Scoring Systems

Diagnostic scoring systems, such as those established by the International Autoimmune Hepatitis Group (IAIHG), can support clinical judgment and serve as valuable tools in diagnosis and research 2, 6

  • These scoring systems are based on several clinical, laboratory, and histological parameters 2

Histological Analysis

Histological analysis remains the cornerstone of AIH diagnosis, with liver biopsy essential to make the diagnosis 6

  • Interface hepatitis with lymphoplasmacellular infiltrates on liver biopsy is a characteristic feature of AIH 4

References

Guideline

Guideline Directed Topic Overview

Dr.Oracle Medical Advisory Board & Editors, 2025

Research

Autoimmune hepatitis.

Nature reviews. Gastroenterology & hepatology, 2011

Research

Diagnosis and therapy of autoimmune hepatitis.

Mini reviews in medicinal chemistry, 2009

Research

Autoimmune hepatitis: a comprehensive review.

Journal of autoimmunity, 2013

Research

Diagnosis of Autoimmune Hepatitis.

Clinics in liver disease, 2024

Professional Medical Disclaimer

This information is intended for healthcare professionals. Any medical decision-making should rely on clinical judgment and independently verified information. The content provided herein does not replace professional discretion and should be considered supplementary to established clinical guidelines. Healthcare providers should verify all information against primary literature and current practice standards before application in patient care. Dr.Oracle assumes no liability for clinical decisions based on this content.

Have a follow-up question?

Our Medical A.I. is used by practicing medical doctors at top research institutions around the world. Ask any follow up question and get world-class guideline-backed answers instantly.