What is the initial workup for hypercalcemia?

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Initial Workup for Hypercalcemia

Measure serum intact parathyroid hormone (PTH) immediately alongside a repeat calcium level (corrected for albumin) to distinguish PTH-dependent from PTH-independent causes—this single test directs all subsequent evaluation. 1, 2

Essential First-Line Laboratory Tests

The initial workup must include:

  • Serum intact PTH (use EDTA plasma for most stable results) 1, 3
  • Corrected total calcium (or ionized calcium if albumin is abnormal) 1, 2
  • Serum phosphate (typically low in hyperparathyroidism, variable in malignancy) 3
  • Comprehensive metabolic panel including creatinine, BUN, and liver function tests 1
  • Serum albumin to properly correct calcium levels 1

PTH-Based Diagnostic Algorithm

If PTH is Elevated or Inappropriately Normal (PTH-Dependent)

This pattern indicates primary hyperparathyroidism in >90% of cases 1, 2:

  • Measure 25-hydroxyvitamin D to exclude vitamin D deficiency as a cause of secondary hyperparathyroidism (must be ruled out before confirming primary hyperparathyroidism) 1, 3
  • 24-hour urine calcium or spot urine calcium/creatinine ratio to assess hypercalciuria and exclude familial hypocalciuric hypercalcemia 1, 3
  • Renal ultrasound to evaluate for nephrocalcinosis or kidney stones 1
  • Bone density scan if chronic hyperparathyroidism is suspected 1

Critical pitfall: Do NOT order parathyroid imaging (ultrasound or sestamibi scan) until biochemical diagnosis is confirmed—imaging is for surgical planning only, not diagnosis 1

If PTH is Suppressed (<20 pg/mL, PTH-Independent)

This pattern suggests malignancy or other non-PTH causes 2, 4:

  • PTH-related peptide (PTHrP) if malignancy suspected (elevated in humoral hypercalcemia of malignancy) 1
  • 1,25-dihydroxyvitamin D (elevated in granulomatous disease, lymphoma, or CYP24A1 mutations) 1, 5
  • 25-hydroxyvitamin D (markedly elevated >150 ng/mL suggests vitamin D intoxication) 1, 5
  • Chest imaging if not already done, to evaluate for malignancy or sarcoidosis 1
  • Serum and urine protein electrophoresis if multiple myeloma suspected 4

Key diagnostic relationships: In PTH-independent hypercalcemia, the suppressed PTH leads to decreased 1,25-dihydroxyvitamin D production (except in granulomatous disease or lymphoma where ectopic CYP27B1 produces excess 1,25-dihydroxyvitamin D despite low PTH) 1, 5

Additional Considerations

  • Medication review: Discontinue thiazide diuretics, calcium supplements, vitamin D supplements, and lithium if present 1, 2
  • Assess severity: Mild hypercalcemia (<12 mg/dL) is often asymptomatic; severe hypercalcemia (≥14 mg/dL) requires urgent treatment 2
  • Monitor frequency: Check calcium and PTH every 3 months initially if observation is chosen 1

Common Pitfalls to Avoid

  • PTH assay variability: Different assays can vary by up to 47%; use assay-specific reference ranges and the same assay for serial measurements 1, 3
  • Biotin interference: Stop biotin supplements 72 hours before PTH testing as they can falsely elevate or decrease results 3
  • Timing matters: PTH has 20% biological variation in healthy individuals; differences must exceed 54% to be clinically significant 1
  • Race and age factors: PTH is 20% higher in Black individuals and increases with age—interpret accordingly 3

When to Refer

Refer to endocrinology and an experienced parathyroid surgeon if primary hyperparathyroidism is confirmed and patient meets surgical criteria (age <50, calcium >1 mg/dL above upper limit, GFR <60 mL/min/1.73 m², nephrolithiasis, or osteoporosis) 1

References

Guideline

Hypercalcemia Diagnosis and Management

Praxis Medical Insights: Practical Summaries of Clinical Guidelines, 2025

Research

Hypercalcemia: A Review.

JAMA, 2022

Guideline

Laboratory Evaluation for Hypercalcemia and Elevated iPTH

Praxis Medical Insights: Practical Summaries of Clinical Guidelines, 2025

Research

Hypercalcemia: an evidence-based approach to clinical cases.

Iranian journal of kidney diseases, 2009

Professional Medical Disclaimer

This information is intended for healthcare professionals. Any medical decision-making should rely on clinical judgment and independently verified information. The content provided herein does not replace professional discretion and should be considered supplementary to established clinical guidelines. Healthcare providers should verify all information against primary literature and current practice standards before application in patient care. Dr.Oracle assumes no liability for clinical decisions based on this content.

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