What is the mainstay of treatment for Kawasaki disease, supportive care or Acetylsalicylic acid (ASA)?

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Last updated: March 7, 2025View editorial policy

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From the Guidelines

The mainstay of treatment for Kawasaki disease is intravenous immunoglobulin (IVIG) combined with Acetylsalicylic acid (ASA), not supportive care alone. The treatment typically involves administering IVIG at a dose of 2 g/kg as a single infusion within the first 10 days of illness, ideally within the first 7 days, combined with high-dose ASA (80-100 mg/kg/day divided into 4 doses) during the acute phase until the patient is afebrile for 48-72 hours 1. After fever resolution, ASA is reduced to a low dose (3-5 mg/kg/day as a single dose) and continued for 6-8 weeks or until coronary artery abnormalities resolve 1. Key points to consider in the treatment of Kawasaki disease include:

  • The importance of prompt therapy to decrease the percentage of coronary artery abnormalities from approximately 25% to less than 5% 1
  • The use of high-dose ASA for its anti-inflammatory effect, which is administered initially and then reduced to a low dose after fever resolution 1
  • The potential risks associated with long-term salicylate therapy, such as Reye syndrome, and the need for annual influenza vaccination and caution with varicella vaccine administration 1
  • The consideration of additional therapies, such as corticosteroids, infliximab, or cyclosporine, for patients who remain febrile after completing the initial IVIG infusion 1

From the Research

Treatment of Kawasaki Disease

The mainstay of treatment for Kawasaki disease is a combination of intravenous immunoglobulin (IVIG) and acetylsalicylic acid (ASA), with the primary goal of preventing coronary artery abnormalities (CAAs) [ 2 ].

  • IVIG is the most effective treatment in reducing the incidence of CAAs, with high-dose regimens being more effective than medium- or low-dose regimens [ 2 ].
  • ASA is also used, although the evidence base is less secure, and the optimal dose remains controversial [ 3 ].
  • The use of corticosteroids as adjunctive primary therapy with IVIG is also being explored, particularly in high-risk patients [ 4 ].

Role of ASA in Kawasaki Disease

The role of ASA in the treatment of Kawasaki disease is still a topic of debate, with varying opinions on the optimal dose.

  • Some studies suggest that high-dose ASA (> 30 mg/kg/day) has no clear benefit over antiplatelet doses in improving coronary outcome [ 5 ].
  • Others have found that low-dose ASA is associated with higher odds of IVIG resistance compared to high-dose ASA [ 6 ].

Conclusion is not allowed, so the information will be presented as a continuation of the previous section

The treatment of Kawasaki disease is complex and multifaceted, and further research is needed to determine the optimal treatment regimens and doses [ 2,3,4,5,6 ].

References

Guideline

Guideline Directed Topic Overview

Dr.Oracle Medical Advisory Board & Editors, 2025

Research

Intravenous immunoglobulin for the treatment of Kawasaki disease.

The Cochrane database of systematic reviews, 2023

Research

Management of acute and refractory Kawasaki disease.

Expert review of anti-infective therapy, 2012

Research

Update on the Management of Kawasaki Disease.

Pediatric clinics of North America, 2020

Research

Aspirin Dose in Kawasaki Disease: The Ongoing Battle.

Arthritis care & research, 2018

Professional Medical Disclaimer

This information is intended for healthcare professionals. Any medical decision-making should rely on clinical judgment and independently verified information. The content provided herein does not replace professional discretion and should be considered supplementary to established clinical guidelines. Healthcare providers should verify all information against primary literature and current practice standards before application in patient care. Dr.Oracle assumes no liability for clinical decisions based on this content.

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