What is the most likely cause of a patient with rheumatoid arthritis (RA) on methotrexate (MTX) developing fever, chills, and mouth ulcers?

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Methotrexate-Induced Neutropenia

The most likely cause is methotrexate-induced neutropenia (Answer A), as the triad of fever, chills, and mouth ulcers (oral mucositis) is the classic presentation of methotrexate-induced bone marrow suppression. 1, 2

Clinical Reasoning

Why Methotrexate-Induced Neutropenia is Most Likely

  • Oral mucositis with fever is the hallmark presentation of MTX-induced pancytopenia. In a case series of 46 patients with MTX-induced pancytopenia, oral mucositis was present in 80% (37/46) and fever in 52% (24/46) of cases. 2

  • The American Academy of Dermatology identifies mucocutaneous effects such as stomatitis and mouth ulcers as very common early toxicities of methotrexate. 1

  • Pancytopenia can occur after even a single dose of methotrexate and can develop at any time during treatment, typically in patients with at least one risk factor. 1

  • The FDA drug label specifically lists "chills and fever" along with "ulcerative stomatitis" and "leukopenia" as the most frequently reported adverse reactions to methotrexate. 3

Why Other Options Are Less Likely

  • Felty syndrome (Answer C) presents with the triad of rheumatoid arthritis, splenomegaly, and neutropenia—but typically develops in patients with long-standing, severe RA with high rheumatoid factor titers. The acute presentation with fever and mouth ulcers points more toward drug toxicity. 1, 2

  • Concomitant SLE (Answer B) would not explain the acute presentation of fever with mouth ulcers in a patient on methotrexate. While oral ulcers occur in SLE, the temporal relationship with MTX therapy and the fever pattern suggest drug toxicity.

  • Viral infection (Answer D) is possible but less likely given the specific constellation of symptoms. While methotrexate increases infection risk, the combination of oral mucositis with fever is more characteristic of bone marrow suppression than simple viral infection. 1, 4

Immediate Management Required

  • Obtain urgent complete blood count with differential to confirm neutropenia. This is the critical first step. 1

  • Discontinue methotrexate immediately if neutropenia is confirmed. 5, 1

  • Initiate leucovorin (folinic acid) rescue therapy if severe bone marrow suppression is present. Leucovorin should be given intravenously at an initial dose of up to 100 mg/m² every 6 hours until hematological abnormalities normalize and mucosal ulceration heals. 5

  • Consider filgrastim (G-CSF) at 5 mcg/kg daily subcutaneously for toxic bone marrow suppression to accelerate myeloid recovery. 5

  • Monitor carefully for signs of sepsis as there is high mortality risk associated with MTX-induced pancytopenia. In the case series, 13 of 46 patients (28%) died, with WBC at admission being the most important prognostic factor. 2

Common Risk Factors to Assess

  • Renal insufficiency is a major modifiable risk factor for MTX-induced myelosuppression. 1

  • Drug interactions, particularly NSAIDs (which decrease renal clearance), trimethoprim-sulfamethoxazole (dual folic acid antagonist), and penicillins. 1, 6

  • Dosing errors, such as daily instead of weekly administration. 1

  • Hypoalbuminemia increases free drug levels. 1, 2

  • Folic acid deficiency or non-supplementation. 1, 2

References

Guideline

Methotrexate Side Effects and Management

Praxis Medical Insights: Practical Summaries of Clinical Guidelines, 2025

Research

Methotrexate-induced pancytopenia: a case series of 46 patients.

International journal of rheumatic diseases, 2017

Guideline

Preventing Infections in Non-Vaccinated Individuals on Methotrexate Therapy

Praxis Medical Insights: Practical Summaries of Clinical Guidelines, 2025

Guideline

Guideline Directed Topic Overview

Dr.Oracle Medical Advisory Board & Editors, 2025

Research

[Side-effects during treatment of rheumatoid arthritis with methotrexate].

Revue du rhumatisme (Ed. francaise : 1993), 1994

Professional Medical Disclaimer

This information is intended for healthcare professionals. Any medical decision-making should rely on clinical judgment and independently verified information. The content provided herein does not replace professional discretion and should be considered supplementary to established clinical guidelines. Healthcare providers should verify all information against primary literature and current practice standards before application in patient care. Dr.Oracle assumes no liability for clinical decisions based on this content.

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