What diagnostic workup is recommended for a patient presenting with a buffalo hump or acanthosis nigricans?

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Diagnostic Workup for Buffalo Hump or Acanthosis Nigricans

Screen immediately for insulin resistance and diabetes with fasting glucose followed by a 2-hour oral glucose tolerance test (75-gram glucose load), as these physical findings are strong markers of metabolic dysfunction. 1, 2

Initial Laboratory Evaluation

Essential Metabolic Screening

  • Fasting plasma glucose followed by 2-hour oral glucose tolerance test (75-gram load) to detect diabetes and impaired glucose tolerance 1, 2
  • Fasting insulin levels (normal <15 mU/L; borderline 15-20 mU/L; high >20 mU/L) to directly assess insulin resistance 3
  • Hemoglobin A1C (values 5.7-6.4% indicate prediabetes) 3
  • Fasting lipid panel including total cholesterol, LDL, HDL, and triglycerides 1, 3

Endocrine Evaluation

  • Thyroid-stimulating hormone (TSH) to exclude thyroid disease 1, 4
  • Total testosterone or free/bioavailable testosterone to evaluate for hyperandrogenism, particularly in women 1
  • Prolactin level if clinical features suggest hyperprolactinemia 1

When Buffalo Hump is Present

If buffalo hump is identified, immediately screen for Cushing's syndrome with appropriate testing (24-hour urinary free cortisol, late-night salivary cortisol, or low-dose dexamethasone suppression test), as this represents a potentially serious endocrine disorder requiring urgent evaluation. 1

Additional considerations for buffalo hump:

  • HIV status and antiretroviral medication history if risk factors present, as HIV-associated lipodystrophy is a common cause 5
  • Duration of HIV infection, viral load, and CD4 counts if HIV-positive 5

Physical Examination Focus

Key Clinical Features to Document

  • Body mass index (BMI) and waist-hip ratio calculation 1
  • Distribution and extent of acanthosis nigricans (neck, axillae, groin, beneath breasts, vulva) 1
  • Signs of hyperandrogenism: acne, hirsutism, male-pattern balding, clitoromegaly 1, 2
  • Signs of Cushing's syndrome: moon facies, hypertension, abdominal striae, centripetal fat distribution, easy bruising, proximal muscle weakness 1
  • Pelvic examination for ovarian enlargement if PCOS suspected 1

Malignancy Screening

In patients with rapidly progressive or extensive acanthosis nigricans, particularly with "tripe palms" (palmar involvement), pursue age-appropriate cancer screening with emphasis on gastric and intra-abdominal malignancies. 1, 6, 7

  • Acanthosis nigricans associated with malignancy most commonly involves gastric adenocarcinoma 1
  • Consider upper endoscopy if rapid onset, extensive disease, or tripe palms present 6
  • In women, evaluate for endometrial cancer risk, especially with obesity, chronic anovulation, and hyperinsulinemia 1, 6
  • Age-appropriate cancer screening based on clinical history and examination 1

Differential Diagnosis Considerations

Polycystic Ovary Syndrome (PCOS)

When acanthosis nigricans occurs with menstrual irregularities or hyperandrogenism in women:

  • Document menstrual history and onset/duration of androgen excess signs 1
  • Exclude other causes: nonclassic congenital adrenal hyperplasia, androgen-secreting tumors, acromegaly 1
  • Screen for type 2 diabetes given demonstrated increased risk in PCOS 1

Pediatric Considerations

In children and adolescents with acanthosis nigricans:

  • Serves as early marker for insulin resistance and type 2 diabetes risk 2
  • Distinguishing type 1 from type 2 diabetes can be challenging, as obesity and acanthosis nigricans may occur with either type 1, 2
  • Consider islet autoantibodies if diabetes type unclear 1

Common Pitfalls

  • Do not assume benign etiology based solely on obesity; always screen for diabetes and other endocrine disorders 4
  • Insulin resistance testing must be performed fasting to avoid postprandial variations 3
  • Rapidly progressive acanthosis nigricans warrants urgent malignancy workup, not reassurance 6, 7
  • Buffalo hump requires Cushing's syndrome exclusion before attributing to obesity alone 1
  • In HIV-positive patients, lipodystrophy changes are often permanent despite antiretroviral modification 5

References

Guideline

Guideline Directed Topic Overview

Dr.Oracle Medical Advisory Board & Editors, 2025

Guideline

Management of Acanthosis Nigricans

Praxis Medical Insights: Practical Summaries of Clinical Guidelines, 2025

Guideline

Diagnosing Insulin Resistance

Praxis Medical Insights: Practical Summaries of Clinical Guidelines, 2025

Guideline

Buffalo Hump in Lipodystrophy Syndromes

Praxis Medical Insights: Practical Summaries of Clinical Guidelines, 2025

Professional Medical Disclaimer

This information is intended for healthcare professionals. Any medical decision-making should rely on clinical judgment and independently verified information. The content provided herein does not replace professional discretion and should be considered supplementary to established clinical guidelines. Healthcare providers should verify all information against primary literature and current practice standards before application in patient care. Dr.Oracle assumes no liability for clinical decisions based on this content.

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