What is the diagnosis for a 4-month-old male infant with macroglossia (enlarged tongue) and unilateral leg hypertrophy?

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Differential Diagnosis for a 4-month-old Boy with Enlarged Tongue and Unilateral Leg Enlargement

  • Single Most Likely Diagnosis
    • Klippel-Trenaunay-Weber syndrome: This condition is characterized by congenital malformations, including hemihypertrophy (enlargement of one side of the body), which could explain the significant difference in leg circumference. The enlarged tongue could be a separate finding or associated with another condition, but given the other symptoms, Klippel-Trenaunay-Weber syndrome is a strong consideration.
  • Other Likely Diagnoses
    • Hemihypertrophy: This condition involves the enlargement of one side of the body and could explain the leg size discrepancy. It can occur in isolation or as part of other syndromes.
    • Beckwith-Wiedemann Syndrome: Characterized by overgrowth, this syndrome can include features like macroglossia (enlarged tongue) and hemihypertrophy, making it a plausible diagnosis given the patient's symptoms.
    • Lymphatic malformation: This could potentially explain the unilateral leg enlargement if there's an underlying lymphatic abnormality causing swelling.
  • Do Not Miss Diagnoses
    • Neurofibromatosis Type 1 (NF1): Although less likely, NF1 can cause hemihypertrophy and other growth abnormalities. Missing this diagnosis could lead to delayed detection of associated serious conditions like optic gliomas.
    • Malignancy (e.g., soft tissue sarcoma): Although rare in this age group, any significant and unexplained asymmetry or growth abnormality warrants consideration of malignancy to ensure prompt diagnosis and treatment.
  • Rare Diagnoses
    • Proteus syndrome: A rare condition characterized by an overgrowth of the skin, bones, and organs, which could potentially explain the findings, though it's much less common.
    • Congenital vascular malformations: These could cause localized overgrowth or swelling, such as in the case of a arteriovenous malformation, but would be less likely to cause the specific combination of findings described.

Professional Medical Disclaimer

This information is intended for healthcare professionals. Any medical decision-making should rely on clinical judgment and independently verified information. The content provided herein does not replace professional discretion and should be considered supplementary to established clinical guidelines. Healthcare providers should verify all information against primary literature and current practice standards before application in patient care. Dr.Oracle assumes no liability for clinical decisions based on this content.

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